Lymphoma is a malignant neoplasm originating from clonal proliferations of monoclonal B-cell, T-cell, and natural killer cell lymphocytes. The ocular adnexa is involved in 2% of extranodal lymphomas, and 5% of these are located in the eyelid. The majority of eyelid and orbital lymphomas are non-Hodgkin B-cell lymphomas. Onset is typically insidious as painless ptosis, eyelid swelling, proptosis, and often a palpable mass. Anterior lesions may present as a salmon-colored subconjunctival mass. Low-grade well-differentiated lesions can be treated with radiotherapy. For less well-differentiated lesions and those with systemic disease, chemotherapy is indicated.